Pancreatic kaposiform hemangioendothelioma complicated by Kasabach–Merritt phenomenon: A rare entity

SA Journal of Radiology

 
 
Field Value
 
Title Pancreatic kaposiform hemangioendothelioma complicated by Kasabach–Merritt phenomenon: A rare entity
 
Creator Mathew, Denny Mahomed, Nasreen
 
Subject Radiology; paediatrics; paediatric surgery; paediatric radiology Radiology; Paediatrics; Paediatric Surgery; Paediatric Radiology; Pancreas Vascular Tumours.
Description Primary pancreatic tumours are a rare and unusual entity in children. In this article, we present the case of an 8-month-old girl who presented with obstructive jaundice. The differential diagnosis based on imaging studies was that of a pancreatic vascular neoplasm; however, with the laboratory evidence of Kasabach–Merritt phenomenon (KMP), this prompted the diagnosis of pancreatic kaposiform hemangioendothelioma. A core biopsy of the pancreatic mass was taken at laparotomy and confirmed this diagnosis. The pancreas is an exceedingly rare site of occurrence for this tumour, with only nine cases being published to date. The clinical, biochemical, imaging and pathological findings are discussed to highlight a rare and potentially life-threatening vascular tumour.
 
Publisher AOSIS
 
Contributor
Date 2019-08-19
 
Type info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion — —
Format text/html application/epub+zip text/xml application/pdf
Identifier 10.4102/sajr.v23i1.1760
 
Source South African Journal of Radiology; Vol 23, No 1 (2019); 5 pages 2078-6778 1027-202X
 
Language eng
 
Relation
The following web links (URLs) may trigger a file download or direct you to an alternative webpage to gain access to a publication file format of the published article:

https://sajr.org.za/index.php/sajr/article/view/1760/2336 https://sajr.org.za/index.php/sajr/article/view/1760/2335 https://sajr.org.za/index.php/sajr/article/view/1760/2337 https://sajr.org.za/index.php/sajr/article/view/1760/2333
 
Coverage — — —
Rights Copyright (c) 2019 Denny Mathew, Nasreen Mahomed https://creativecommons.org/licenses/by/4.0
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